《罕见原发性肝癌：欧洲肝病学会立场报告》摘译
| 作 者：European Association for the Study of the Liver, 蒋晓玲 |
| 单 位：上海交通大学医学院附属仁济医院 上海市消化疾病研究所 |
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| 摘 要： |
| 近年来，随着对肝癌发病分子机制理解的不断深入，以及原发性肝癌（PLC）治疗选择的进展，包括混合型肝细胞癌-胆管细胞癌、纤维板层癌、肝上皮样血管内皮瘤等在内的罕见PLC受到越来越多的关注。这篇立场报告中，由肿瘤学、肝病学、病理学、影像学和外科学领域专家组成的国际专家小组采用系统方法总结了关于罕见PLC发病机制、诊断和治疗的可用信息和证据。虽然针对一些罕见PLC系统治疗的临床试验正在开展中，但仍需要更多国家和国际合作层面的研究提供循证医学证据。 |
| 关键词：罕见原发性肝癌；肝细胞癌-胆管细胞癌；纤维板层癌；肝细胞腺瘤；肝上皮样血管内皮瘤 |
Key Points in Rare Primary Liver Cancers: An EASL Position Paper
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| Abstract: |
| In recent years, owing to advances in understanding of the hepatocarcinogenesis and treatment options, rare primary liver cancers (PLC), including hepatocellular-cholangio-carcinoma, fibrolamellar carcinoma, and hepatic epithelioid hemangioendothelioma have garnered increased attention. In this position paper, an international panel of experts representing oncology, hepatology, pathology, radiology, and surgery systematically summarized the available information and evidence on pathogenesis, diagnosis, and treatment of these rare PLCs. While clinical trials of systemic treatments are underway for some rare PLCs, more researches, involving national and international collaboration are required to provide evidence-based medicine evidence. |
| Keywords: Rare Primary Liver Cancer; Hepatocellular-Cholangio-Carcinoma; Fibrolamellar Carcinoma; Hepatocellular Adenoma; Hepatic Epithelioid Hemangioendothelioma; Hepatic Angiosarcoma |
| 投稿时间：2026-02-08 |
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